Plasminogen deficiency type 1 (PLGD-1) is an ultra-rare genetic disorder that affects the body’s ability to break down fibrin. This leads to complications such as abnormal wound healing and tissue growth. It typically impacts the eyes, respiratory tract, and other mucous membranes.

PLGD-1 leads to reduced plasminogen activity levels in the body, often resulting in fibrinous lesions on various organs. Approximately 81% of patients develop lesions on one or both eyes as their primary symptom; however, lesions can develop throughout the body, potentially on all organs with mucous membranes. Patients with PLGD-1 may require lifelong treatment.

Adult Woman and Adult Man

Diagnosis of Plasminogen Deficiency Type 1

Diagnosing plasminogen deficiency type 1 (PLGD-1) involves a combination of clinical evaluation and laboratory testing.

A healthcare provider may first assess the characteristic symptoms, such as ligneous conjunctivitis or mucous membrane lesions.

The definitive diagnosis is made through blood tests that measure the activity and levels of plasminogen.

Genetic testing can also be performed to identify mutations in the PLG gene, which confirms the diagnosis of PLGD-1.

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Symptoms of Plasminogen Deficiency

Plasminogen deficiency symptoms can vary but often include:

  • Eye lesions, called ligneous conjunctivitis (LC)
  • Impaired wound healing
  • Respiratory problems due to tissue build-up in airways
  • Swelling of mucous membranes

Plasminogen Deficiency Treatment

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RYPLAZIM® is the first and only Food & Drug Administration (FDA) approved treatment for supporting the approximately 500 people in the U.S. affected by plasminogen deficiency type 1 (PLGD-1).  RYPLAZIM helps restore plasminogen levels, addressing the root cause of symptoms.

RYPLAZIM Website


Soleo Health is among the few specialty pharmacy providers selected to administer RYPLAZIM to PLGD-1 patients. Our clinical team works with patients and their healthcare providers to ensure the best outcomes. We offer ongoing support, education, and assistance with RYPLAZIM prescribing information and insurance coverage.

Start a PLGD-1 Referral

RYPLAZIM Patient Story

What began as persistent coughing in a young child evolved into a complex medical mystery that took years to solve. This is the story of Wren, a Soleo Health patient, and her parents’ determination to find answers.

After consulting with 15 different specialists without answers, the family finally found their way to genetics. The decision to map Wren’s exome proved to be the key, revealing a diagnosis of Plasminogen deficiency type 1 (PLGD-1), which doctors described as “finding a needle in a haystack.”

This story highlights the importance of persistent advocacy, the value of genetic testing in complex cases, and the reality that rare diseases like PLGD-1 don’t always present in textbook ways.

Our Dedicated PLGD-1 Management Program Provides

 

• Education by RYPLAZIM-certified trained staff • Clinical support and adherence management
• Personalized care plan for each patient • Dedicated patient ambassadors
• Health insurance coordination and support • Co-pay assistance for RYPLAZIM
• 24/7 availability of clinical support • Customized outcome reporting, upon request

Patient Support

Patient Advocacy

Patient advocates provide support by answering insurance questions, helping with family issues, offering information about Medical IDs, and assisting with health coverage concerns.

Patient Education

Our team offers comprehensive support and education for patients, their families, and caregivers throughout treatment.

Peer to Peer Support

Our patient advocates can connect you with resources for peer-to-peer discussions about medication dosage and frequency.

Referrals

Soleo Health appreciates the opportunity to treat specialty therapy patients. We have a simple referral process to help providers get their patients started.

24/7/365 Patient Care Support

We have experienced pharmacists and registered nurses who can assist with your care and concerns

National Nursing Coverage

We have pharmacy licensure in all 50 states and national nursing coverage. We can care for you no matter where you live

Flexible Site of Care Options

We can provide services in your home, physician's office or at one of our many infusion centers.